Inflammatory Myofibroblastic Tumor of the Esophagus in Childhood: A Case Report and a Review of the Literature. Issue 2 (March 2015)

• Record Type: Journal Article
• Authors: Dousek, Robert; Tuma, Jiri; Planka, Ladislav; Husek, Karel; Sterba, Jaroslav; Penka, Igor
• Is Part Of: Journal of pediatric hematology/oncology. Volume 37:Issue 2(2015)
• Publication Date: 2015-03
• Subjects: inflammatory myofibroblastic tumor -- esophagus -- pediatric surgery; Pediatric hematology -- Periodicals; Tumors in children -- Periodicals; 618.9215
• DOI: 10.1097/MPH.0000000000000275
• Languages: English
• ISSNs: 1077-4114

Abstract

Abstract : Inflammatory myofibroblastic tumor (IMT) is a rare mesenchymal disease of low malignancy consisting of inflammatory cells inside a mesenchymal stroma comprising myofibroblasts. Biological behavior is variable, recurrence is uncommon, metastatic disease is rare. Treatment strategy is based on the status of low-grade malignant tumor. Radical surgery is considered to be the principal treatment modality, except if it requires a mutilating procedure. Only 6 cases of pediatric patients treated for IMT of the esophagus have been reported in English-language literature. Herein, a case of a 13-year-old boy with an IMT of the esophagus is presented.