Sonography used in the infantile desmoid fibromatosis of postcricoid area: A case report. Issue 44 (November 2017)

• Record Type: Journal Article
• Authors: Xia, Chunxia; Zhu, Qiang; Yue, Changli; Hu, Minxia; Li, Pingdong; Li, Zheng
• Other Names: Efird. Jimmy T. section editor.
• Is Part Of: Medicine. Volume 96:Issue 44(2017)
• Publication Date: 2017-11
• Subjects: desmoid fibromatosis -- hypopharynx -- infantile -- sonography -- tumors; Medicine -- Periodicals; Medicine -- Periodicals; Médecine -- Périodiques; Geneeskunde; Medicine; Periodicals; Periodicals; 610.5
• DOI: 10.1097/MD.0000000000008500
• Languages: English
• ISSNs: 0025-7974

Abstract

Abstract: Rationale: Infantile desmoid fibromatosis of the postcricoid area is a rare disease and is characterized by a proliferation of fibrous tissue with non-metastasis, local infiltration, and a high rate of recurrence after surgical resection. Currently, ultrasound is scarcely used in the hypopharynx and larynx area. Patient concerns: A 4-year-old boy presented with hoarseness, deep voice and snoring for 2∼4 years without any surgical history. On sonography, the lesion was found in the postcricoid area, and the left larynx showed impaired mobility in real time observation. Complete excision with a negative margin in this pivotal anatomic area is impossible, and necessitates a long-time surveillance. Diagnoses: Infantile desmoid fibromatosis of the postcricoid area was diagnosed according to surgery and histopathology. Interventions: Local excision was carried out to relieve the upper airway narrowing. Outcomes: Relieved hoarseness and snoring were reported on the latest follow-up. A residual lesion was seen in the surgical bed and maintained a stable extent on ultrasound and MR imaging after a year. Lessons: Considering the non-radiation merit and diagnostic ability, ultrasonography is advocated as a valuable supplementary imaging method to CT, MR and laryngoscopy in the juvenile larynx and hypopharynx.