Kikuchi-Fujimoto's disease associated with systemic lupus erythematous: difficult case report and literature review. (August 2014)

• Record Type: Journal Article
• Authors: Ruaro, B; Sulli, A; Alessandri, E; Fraternali-Orcioni, G; Cutolo, M
• Is Part Of: Lupus. Volume 23:Number 9(2014)
• Page Start: 939
• Page End: 944
• Publication Date: 2014-08
• Subjects: Kikuchi–Fujimoto's disease -- histiocytic necrotizing lymphadenitis -- systemic lupus erythematosus; Systemic lupus erythematosus -- Periodicals; 616.772005
• DOI: 10.1177/0961203314530794
• Languages: English
• ISSNs: 0961-2033

Abstract

Kikuchi–Fujimoto's disease (KFD), or histiocytic necrotizing lymphadenitis, is a benign and self-limiting disease of unknown aetiology. KFD tends to affect a young population under 30 years of age and predominantly females. KFD is a rare pathology and its association with systemic lupus erythematosus (SLE) is not frequent. Herein, we present the case of a male Italian patient with SLE in association with KFD with 5 years of follow-up, where a differential diagnosis from infection or lymphoproliferative disease was problematic.