Adenoid cystic carcinoma of the lacrimal gland in a 14-year-old male. (2nd November 2017)

• Record Type: Journal Article
• Authors: Falcone, Michelle M.; Tran, Kimberly D.; Tavakoli, Mehdi; Ortiz, Daniel F.; Barredo, Julio C.; Lee, Wendy W.
• Is Part Of: Orbit. Volume 36:Number 6(2017)
• Page Start: 448
• Page End: 451
• Publication Date: 2017-11-02
• Subjects: Adenoid cystic carcinoma -- intra-arterial chemotherapy -- lacrimal gland -- pediatric; Eye-sockets -- Surgery -- Periodicals; Eye-sockets -- Diseases -- Periodicals; Orbit -- surgery -- Periodicals; Orbital Diseases -- Periodicals; 617.7
• DOI: 10.1080/01676830.2017.1337187
• Languages: English
• ISSNs: 0167-6830

Abstract

ABSTRACT: Adenoid cystic carcinoma (ACC) of the lacrimal gland is an aggressive, malignant epithelial neoplasm. This tumor is rarely seen in adults and even less commonly seen in children and adolescents; thus, there have been no large studies to date describing the optimal treatment of this malignancy in the pediatric population. Here, we report a case of lacrimal gland ACC in a 14-year-old male treated with neoadjuvant intra-arterial chemotherapy followed by globe-sparing tumor resection and chemoradiation. At 2-year follow-up, he remains disease free without evidence of tumor recurrence.