Large intrathoracic meningocele in a patient with neurofibromatosis type 1. (February 2014)

• Record Type: Journal Article
• Authors: Zuo, Tao; Ni, Zhengyi; Zhou, Mi; Huang, Chaolin; Tang, Zhongwen; Yang, Zhifeng
• Is Part Of: Asian cardiovascular & thoracic annals. Volume 22:Number 2(2014)
• Page Start: 219
• Page End: 221
• Publication Date: 2014-02
• Subjects: Cafe-au-lait spots -- Meningocele -- Nervous system diseases -- Nervous system neoplasms -- neurofibromatosis 1; Heart -- Diseases -- Asia -- Periodicals; Heart -- Diseases -- Pacific Area -- Periodicals; Heart -- Diseases -- Periodicals; Heart -- Surgery -- Asia -- Periodicals; Heart -- Surgery -- Pacific Area -- Periodicals; Heart -- Surgery -- Periodicals; Chest -- Surgery -- Asia -- Periodicals; Chest -- Surgery -- Pacific Area -- Periodicals; Chest -- Surgery -- Periodicals; 617.412
• DOI: 10.1177/0218492312475293
• Languages: English
• ISSNs: 0218-4923

Abstract

Intrathoracic meningocele associated with neurofibromatosis type 1 is quite rare. We report the case of a Chinese women with a 20-day history of right-sided chest pain and sense of pressure on the chest. Computed tomography and magnetic resonance imaging indicated a homogeneous thin-walled cystic mass in the right rear mediastinum, ranging from the 1st to 5th thoracic segments. Surgery was performed to removal the meningomyelocele pouches and shunt the cyst to the subarachnoid region.