Aortic surgery in Marfan patients with severe pectus excavatum. Issue 5 (May 2017)

• Record Type: Journal Article
• Authors: Raffa, Giuseppe Maria; Kowalewski, Mariusz; Malvindi, Pietro Giorgio; Bertani, Alessandro; Romano, Giuseppe; Sciacca, Sergio; Turrisi, Marco; Armaro, Alessandro; Stringi, Vincenzo; Montalbano, Giuseppe; Mattiucci, Gabriella; Follis, Fabrizio; Pilato, Michele
• Is Part Of: Journal of cardiovascular medicine. Volume 18:Issue 5(2017:May)
• Publication Date: 2017-05
• Subjects: aortic aneurysm -- heart displacement -- Marfan syndrome -- open-heart surgery -- pectus excavatum; Cardiology -- Periodicals; Cardiovascular system -- Diseases -- Periodicals; Cardiology -- Periodicals; Cardiovascular Diseases -- Periodicals; 616.1005
• DOI: 10.2459/JCM.0000000000000394
• Languages: English
• ISSNs: 1558-2027

Abstract

Abstract : Aims: The optimal surgical management of the aortic root phenotype Marfan patients with severe pectus excavatum is a subject of debate. All the available literature were reviewed according to preferred reporting items for systematic reviews and meta-analyses (PRISMA) principles in order to assess the early outcomes of both pectus excavatum and aortic repair techniques. Methods: Searches were done in PubMed and MEDLINE electronic databases dating from July 1953 to December 2015. Results: A total of 97 peer-reviewed publications were retrieved, and 27 relevant publications were identified with a total of 39 Marfan patients with pectus excavatum who underwent ascending aorta and aortic root surgery. Emergency acute Type-A aortic dissection repair was reported in five cases. Concomitant pectus excavatum and aortic root repair and composite graft implantation were the most commonly performed procedures. Complications after a staged or a combined approach were uncommon and no deaths occurred. Conclusion: Aortic surgery in Marfan patients with pectus excavatum was carried out according to a variety of strategies, surgical techniques and accesses with low complications rate and no mortality. Many of these were well tolerated with minimal complications and no mortality. Abstract : Supplemental Digital Content is available in the text