Surgical Management of Gorlin Syndrome: A 4-Decade Experience Using Local Excision Technique. Issue 4 (April 2015)

• Record Type: Journal Article
• Authors: Griner, Devan; Sutphin, Daniel; Sargent, Larry A.
• Is Part Of: Annals of plastic surgery. Volume 74:Issue 4(2015:Apr.)
• Publication Date: 2015-04
• Subjects: basal cell nevus syndrome -- Gorlin syndrome -- Mohs micrographic surgery; Surgery, Plastic -- Periodicals; 617.95205
• DOI: 10.1097/SAP.0000000000000052
• Languages: English
• ISSNs: 0148-7043

Abstract

Abstract : Abstract: Basal cell nevus syndrome (aka Gorlin syndrome, Gorlin-Goltz syndrome, nevoid basal cell carcinoma syndrome, and fifth phacomatosis) is a rare but well-described autosomal dominant condition with variable penetrance. We present a female patient who has been successfully treated using local surgical excision and diligent skin surveillance for more than 4 decades, demonstrating that simple local incision is an efficacious and reasonable surgical alternative that may circumvent the specialization and expense of Mohs technique.