Anterior Cranial Vault Distraction for the Treatment of Normocephalic Pancraniosynostosis. Issue 3 (May 2016)

• Record Type: Journal Article
• Authors: Wong, Shannon; Nagengast, Eric S.; Miller, Jason
• Is Part Of: Journal of craniofacial surgery. Volume 27:Issue 3(2016)
• Publication Date: 2016-05
• Subjects: Cranial vault expansion -- craniosynostosis -- distraction osteogenesis -- Normocephalic pancraniosynostosis -- pancraniosynostosis; Facial bones -- Surgery -- Periodicals; Skull -- Surgery -- Periodicals; Face -- Surgery -- Periodicals; Surgery, Plastic -- Periodicals; 617.52
• DOI: 10.1097/SCS.0000000000002452
• Languages: English
• ISSNs: 1049-2275

Abstract

Abstract : Abstract: Normocephalic pancraniosynostosis is a rare form of craniosynostosis that usually presents later in life secondary to a delayed onset of symptoms and the presence of a normal head shape. Since its initial description in the literature in 2010, normocephalic pancraniosynostosis remains a rare clinical entity that has only been reported in 6 patients. Surgical treatment in the 2 published reports has been by staged total calvarial reconstruction or anterior cranial vault remodeling with bilateral frontoorbital advancement. In this case report, the authors present 1 patient with normocephalic pancraniosynostosis and propose surgical treatment by anterior cranial vault expansion with distraction osteogenesis.