Cognitive Abilities of Children With Neurological and Liver Forms of Wilson Disease. Issue 3 (March 2017)

• Record Type: Journal Article
• Authors: Favre, Emilie; Lion-François, Laurence; Canton, Marie; Vanlemmens, Claire; Bonneton, Marjorie; Bouillet, Lise; Brunet, Anne-Sophie; Lachaux, Alain
• Is Part Of: Journal of pediatric gastroenterology and nutrition. Volume 64:Issue 3(2017)
• Publication Date: 2017-03
• Subjects: cognitive abilities -- executive function -- liver -- pediatric -- Wilson disease -- working memory; Children -- Nutrition -- Periodicals; Pediatric gastroenterology -- Periodicals; Infants -- Nutrition -- Periodicals; Nutrition disorders in children -- Periodicals; Child Nutrition -- Periodicals; Digestive System -- growth & development -- Periodicals; Gastrointestinal Diseases -- Periodicals; Infant Nutrition -- Periodicals; Nutrition Disorders -- Periodicals; Child; 618.923
• DOI: 10.1097/MPG.0000000000001346
• Languages: English
• ISSNs: 0277-2116

Abstract

Abstract : ABSTRACT: Cognitive impairment in adult patients experiencing Wilson disease is now more clearly described, even in liver forms of the disease. Although this condition can appear during childhood, the cognitive abilities of children have not yet been reported in a substantial case series. This retrospective study included 21 children with Wilson disease who had undergone general cognitive assessment. The results argue in favor of a poor working memory capacity in the liver form of the disease, and more extensive cognitive impairments in its neurological form. Extensive neuropsychological investigations on all children experiencing Wilson disease are thus required. Abstract : Supplemental Digital Content is available in the text