Erdheim–Chester disease: A rare cause of recurrent fever of unknown origin mimicking lymphoma. (January 2014)

• Record Type: Journal Article
• Authors: Mariampillai, Anusiyanthan; Sivapiragasam, Abirami; Kumar, Amit; Hindenburg, Alexander; Cunha, Burke A.; Zhou, Jianhong
• Is Part Of: Scandinavian journal of infectious diseases. Volume 46:Number 1(2014:Jan.)
• Page Start: 76
• Page End: 79
• Publication Date: 2014-01
• Subjects: Recurrent FUO -- histiocytic disorders -- non-Langerhans cell histiocytosis -- infiltrative bone lesions; Communicable diseases -- Periodicals; Infection -- Periodicals; 616.9
• DOI: 10.3109/00365548.2013.844352
• Languages: English
• ISSNs: 0036-5548

Abstract

Abstract: We report the case of a patient with recurrent fever of unknown origin (FUO) with prominent back pain, hepatosplenomegaly, and abdominal/pelvic adenopathy suggesting lymphoma. A bone biopsy showed histiocytic infiltration. Studies for lymphoma were negative, but immunohistochemical stains were diagnostic of Erdheim–Chester disease (ECD). ECD should be included as a rare cause of recurrent FUO with bone involvement.