Partial anomalous pulmonary venous return in Turner syndrome. Issue 95 (October 2017)

• Record Type: Journal Article
• Authors: van den Hoven, Allard T.; Chelu, Raluca G.; Duijnhouwer, Anthonie L.; Demulier, Laurent; Devos, Daniel; Nieman, Koen; Witsenburg, Maarten; van den Bosch, Annemien E.; loeys, Bart L.; van Hagen, Iris M.; Roos-Hesselink, Jolien W.
• Is Part Of: European journal of radiology. Issue 95(2017)
• Page Start: 141
• Page End: 146
• Publication Date: 2017-10
• Subjects: PAPVR -- Turner syndrome -- Computed tomography -- PAPVC; Medical radiology -- Periodicals; Radiology -- Periodicals; Radiologie médicale -- Périodiques; Medical radiology; Periodicals; 616.075705
• DOI: 10.1016/j.ejrad.2017.07.024
• Languages: English
• ISSNs: 0720-048X

Abstract

Abstract: Purpose: The aim of this study is to describe the prevalence, anatomy, associations and clinical impact of partial anomalous pulmonary venous return in patients with Turner syndrome. Methods and results: All Turner patients who presented at our Turner clinic, between January 2007 and October 2015 were included in this study and underwent ECG, echocardiography and advanced imaging such as cardiac magnetic resonance or computed tomography as part of their regular clinical workup. All imaging was re-evaluated and detailed anatomy was described. Partial anomalous pulmonary venous return was diagnosed in 24 (25%) out of 96 Turner patients included and 14 (58%) of these 24 partial anomalous pulmonary venous return had not been reported previously. Right atrial or ventricular dilatation was present in 11 (46%) of 24 partial anomalous pulmonary venous return patients. Conclusion: When studied with advanced imaging modalities and looked for with specific attention, PAPVR is found in 1 out of 4 Turner patients. Half of these patients had right atrial and/or ventricular dilatation. Evaluation of pulmonary venous return should be included in the standard protocol in all Turner patients.