Diffuse Elevated Abdominal Activity on 99mTc-Labeled Red Blood Cell Imaging in a Pediatric Patient With Klippel Trenaunay Syndrome. (November 2016)

• Record Type: Journal Article
• Authors: Kaplan, Summer L.; Zhuang, Hongming
• Is Part Of: Clinical nuclear medicine. Volume 41:Number 11(2016)
• Publication Date: 2016-11
• Subjects: Klippel Trenaunay syndrome -- 99mTc red blood cell scintigraphy; Nuclear medicine -- Periodicals; Radioisotope scanning -- Periodicals; Nuclear Medicine -- Periodicals; 616.07575
• DOI: 10.1097/RLU.0000000000001366
• Languages: English
• ISSNs: 0363-9762

Abstract

Abstract : Abstract: Klippel Trenaunay syndrome commonly manifests as lower limb hypertrophy where vascular malformation occurs. However, up to 20% of patients with Klippel Trenaunay syndrome can have gastrointestinal involvement. An 18-year-old man with known Klippel Trenaunay syndrome in the left lower extremity underwent 99m Tc-labeled red blood cell imaging to determine the site of gastrointestinal bleeding. The images did not reveal the site of active bleeding. However, diffuse non-moving activity in the left abdomen and pelvis was noted, which corresponded to hypertrophied colon and related blood vessels, consistent with intestinal involvement of Klippel Trenaunay syndrome.