Mounier–Kuhn syndrome: a case of tracheal smooth muscle remodeling. Issue 2 (29th December 2016)

• Record Type: Journal Article
• Authors: Cook, Daniel P.; Adam, Ryan J.; Abou Alaiwa, Mahmoud H.; Eberlein, Michael; Klesney‐Tait, Julia A.; Parekh, Kalpaj R.; Meyerholz, David K.; Stoltz, David A.
• Is Part Of: Clinical case reports. Volume 5:Issue 2(2017)
• Page Start: 93
• Page End: 96
• Publication Date: 2016-12-29
• Subjects: Airway remodeling -- airway smooth muscle -- Mounier–Kuhn syndrome -- tracheobronchomalacia; Medicine -- Periodicals; 616.09
• DOI: 10.1002/ccr3.794
• Languages: English
• ISSNs: 2050-0904

Abstract

Key Clinical Message: Mounier–Kuhn syndrome is a rare clinical disorder characterized by tracheobronchial dilation and recurrent lower respiratory tract infections. While the etiology of the disease remains unknown, histopathological analysis of Mounier–Kuhn airways demonstrates that the disease is, in part, characterized by cellular changes in airway smooth muscle. Abstract : Mounier–Kuhn syndrome is a rare clinical disorder characterized by tracheobronchial dilation and recurrent lower respiratory tract infections. While the etiology of the disease remains unknown, histopathological analysis of Mounier–Kuhn airways demonstrates that the disease is, in part, characterized by cellular changes in airway smooth muscle.