Minimally invasive endoscopic treatment for pediatric combined high grade stenosis as a laryngeal manifestation of epidermolysis bullosa. (January 2017)

• Record Type: Journal Article
• Authors: Palinko, Dora; Matievics, Vera; Szegesdi, Ilona; Sztano, Balazs; Rovo, Laszlo
• Is Part Of: International journal of pediatric otorhinolaryngology. Volume 92(2017:Jan.)
• Page Start: 126
• Page End: 129
• Publication Date: 2017-01
• Subjects: Epidermolysis bullosa -- CO2 laser -- Commissure stenosis -- Minimally invasive laryngo-microsurgery -- Arytenoid abduction lateropexy -- Pediatric airway stenosis; Otolaryngology -- Periodicals; Pediatrics -- Periodicals; Otolaryngology -- Periodicals; Pediatrics -- Periodicals; Oto-rhino-laryngologie -- Périodiques; Pédiatrie -- Périodiques; 618.9209751
• DOI: 10.1016/j.ijporl.2016.11.020
• Languages: English
• ISSNs: 0165-5876

Abstract

Abstract: Epidermolysis bullosa refers to a clinically and genetically heterogeneous group of inherited mucocutaneous diseases. Laryngotracheal lesions are momentous regarding the risk of sudden airway obstruction. The traditional treatment is tracheostomy. This case report highlights the advantages of minimally invasive interventions. A successful combined endoscopic management of a life-threatening respiratory crisis is presented in a 4-year-old child. Combined commissure stenosis with supraglottic spread was treated by CO2 laser dissection and bilateral endoscopic arytenoid abduction lateropexy, supplemented with mitomycin C application. Due to expectable less scarring, the combination of these modern methods may be an efficient solution in these vulnerable respiratory tracts.