Sialodochitis fibrinosa (kussmaul disease) report of 3 cases and literature review. Issue 42 (October 2016)

• Record Type: Journal Article
• Authors: Flores Robles, Bryan Josue; Brea Álvarez, Beatriz; Sanabria Sanchinel, Abel Alejandro; Andrus, Robert Francis; Espinosa Malpartida, María; Ramos Giráldez, Consuelo; Lerma Verdejo, Ana; Merino Argumanez, Carolina; Pérez Pimiento, Jose Antonio; Bellas Menéndez, Camen; Villa Alcázar, Luis Fernando; Andréu Sánchez, José Luis; Jiménez Palop, Mercedes; Godoy Tundidor, Hildegarda; Campos Esteban, José; Sanz Sanz, Jesús; Barbadillo Mateos, Carmen; Isasi Zaragoza, Carlos María; Mulero Mendoza, Juan Bartolomé
• Other Names: Tobouti. Priscila Lie section editor.
• Is Part Of: Medicine. Volume 95:Issue 42(2016)
• Publication Date: 2016-10
• Subjects: allergic parotitis -- Fibrinous sialodochitis -- Kussmaul disease -- sialodochitis fibrinosa; Medicine -- Periodicals; Medicine -- Periodicals; Médecine -- Périodiques; Geneeskunde; Medicine; Periodicals; Periodicals; 610.5
• DOI: 10.1097/MD.0000000000005132
• Languages: English
• ISSNs: 0025-7974

Abstract

Abstract: Background: Sialodochitis fibrinosa is a rare disease which is characterized by recurring episodes of pain and swelling of the salivary glands due to the formation of mucofibrinous plugs. Analytic studies ascertain elevated levels of eosinophils and immunoglobulin E (IgE). Imaging studies such as magnetic resonance imaging (MRI) and sialography reveal dilation of the main salivary duct (duct ectasia). Treatment is initially supportive, consisting of compressive massages, and use of antihistamines and/or corticosteroids. Material and methods: In the following, 3 cases of sialodochitis fibrinosa are presented which were diagnosed in a third level hospital during the period of 2008 and 2016, as well as a literature review of all cases reported to our knowledge. Results: Of the 41 cases found, including the 3 of this article, 66% were women with an average age of 45 years old. However, 75% of reported cases were of Japanese heritage. Involvement of the parotid glands was more frequent than the submandibular glands. In more than half of all cases treatment with compressive massages, antihistamines and/or corticosteroids was effective. Conclusion: Clinicians should consider sialodochitis fibrinosa as a diagnostic possibility when presented with cases of recurring parotid and submandibular gland tumescence.