The Congenital Heart Surgeons' Society Registry of Anomalous Aortic Origin of a Coronary Artery: an update*. (December 2015)

• Record Type: Journal Article
• Authors: Brothers, Julie A.; Gaynor, J. William; Jacobs, Jeffrey P.; Poynter, Jeffrey A.; Jacobs, Marshall L.
• Is Part Of: Cardiology in the young. Volume 25:Number 8(2015)
• Page Start: 1567
• Page End: 1571
• Publication Date: 2015-12
• Subjects: Congenital cardiac disease, -- paediatric cardiac disease, -- interarterial coronary artery, -- intramural coronary artery, -- intraconal coronary artery; Pediatric cardiology -- Periodicals; 618.9212
• DOI: 10.1017/S1047951115002061
• Languages: English
• ISSNs: 1047-9511

Abstract

Abstract: The anomalous aortic origin of a coronary artery from the wrong sinus of Valsalva with an interarterial, intramural, and/or intraconal course is a relatively rare congenital defect of the heart that may be associated with an increased risk of ischaemia of the myocardium and sudden death, notably in children and young adults. Data are limited regarding stratification of risk and long-term outcomes of these patients. In 2009, the Anomalous Coronary Artery Working Group formed the Congenital Heart Surgeons' Society Registry of Anomalous Aortic Origin of a Coronary Artery to obtain information on large numbers of young patients with anomalous aortic origin of a coronary artery with the goal to better understand the natural and surgical history of this anomaly as well as to develop evidence-based treatment and management guidelines. In this report, we describe the data we have collected from the registry and the current state of the registry.