Congenital afibrinogenemia: a case report of a spontaneous hepatic hematoma. Issue 28 (July 2016)

• Record Type: Journal Article
• Authors: Malaquin, Stephanie; Rebibo, Lionel; Chivot, Cyril; Badoux, Louise; Mahjoub, Yazine; Dupont, Herve
• Other Names: Marchi. Rita section editor.
• Is Part Of: Medicine. Volume 95:Issue 28(2016)
• Publication Date: 2016-07
• Subjects: congenital afibrinogenemia -- hemorrhagic shock -- spontaneous hepatic hematoma; Medicine -- Periodicals; Medicine -- Periodicals; Médecine -- Périodiques; Geneeskunde; Medicine; Periodicals; Periodicals; 610.5
• DOI: 10.1097/MD.0000000000004150
• Languages: English
• ISSNs: 0025-7974

Abstract

Abstract: Introduction: Afibrinogenemia is a rare coagulation disorder. Clinical features of spontaneous bleeding, bleeding after minor trauma, or after surgery have been described as well as thrombo-embolic complications. In this article, we presented the case of a 19-year old female with congenital afibrinogenemia who was admitted with a spontaneous intrahepatic hematoma. Conclusions: Supportive treatment including transfusion and fibrinogen administration, associated with repeated packing surgeries and selective embolization, were successfully performed.