Anesthetic considerations in a parturient with Freeman–Sheldon syndrome. (August 2016)

• Record Type: Journal Article
• Authors: Fisher, K.; Qasem, F.; Armstrong, P.; McConachie, I.
• Is Part Of: International journal of obstetric anesthesia. Volume 27(2016)
• Page Start: 81
• Page End: 84
• Publication Date: 2016-08
• Subjects: Freeman–Sheldon syndrome -- Cesarean delivery -- Anesthesia -- Combined spinal–epidural; Obstetrics -- Periodicals; Anesthesia -- Periodicals; Anesthésie en obstétrique -- Périodiques; Anesthesia; Obstetrics; Electronic journals; Periodicals; 617.9682
• DOI: 10.1016/j.ijoa.2016.02.001
• Languages: English
• ISSNs: 0959-289X

Abstract

Abstract : Highlights: We discuss anesthesia for cesarean delivery in a patient with Freeman Sheldon syndrome. Difficulty with intubation and intravenous access has been reported. Malignant hyperthermia is a potential complication. Multidisciplinary cooperation is essential in managing these patients. Abstract: Freeman–Sheldon syndrome is a rare genetic disorder characterized by malformations of the face, oral cavity and musculoskeletal system. This case report describes the anesthetic management of a parturient with Freeman–Sheldon syndrome, kyphoscoliosis and a cardiac pacemaker for a cesarean delivery and tubal ligation. With a predicted difficult airway, our team decided to provide a combined spinal–epidural anesthetic. Problems encountered included difficult intravenous access, failure to identify the subarachnoid space and patient discomfort during surgery.