Pleuroparenchymal fibroelastosis in association with carcinomas. Issue 1 (13th October 2015)

• Record Type: Journal Article
• Authors: Baroke, Eva; Heussel, Claus Peter; Warth, Arne; Eichinger, Monika; Oltmanns, Ute; Palmowski, Karin; Herth, Felix J.F.; Kreuter, Michael
• Is Part Of: Respirology. Volume 21:Issue 1(2016)
• Page Start: 191
• Page End: 194
• Publication Date: 2015-10-13
• Subjects: cancer -- interstitial lung disease -- lung fibrosis -- pleuroparenchymal fibroelastosis; Respiratory organs -- Diseases -- Periodicals; Respiratory organs -- Periodicals; 612.2
• DOI: 10.1111/resp.12654
• Languages: English
• ISSNs: 1323-7799

Abstract

Abstract : PPFE is a rare disease characterized by upper lobe pleural fibrosis and parenchymal fibroelastosis. Its aetiology is considered idiopathic, although possible causative factors have been described. An association of PPFE with solid tumours is unknown and has not been considered previously. We identified six patients with PPFE, four of them with a coexisting malignancy. The case series suggests that PPFE might be an implication of varying factors rather than being an exclusively idiopathic condition.