Mondini dysplasia with recurrent bacterial meningitis caused by three different pathogens. Issue 6 (5th November 2015)

• Record Type: Journal Article
• Authors: Shikano, Hiroaki; Ohnishi, Hidenori; Fukutomi, Hisashi; Ito, Kimiko; Morimoto, Masahiro; Teramoto, Takahide; Aoki, Mitsuhiro; Nishihori, Takezumi; Akeda, Yukihiro; Oishi, Kazunori; Fukao, Toshiyuki
• Is Part Of: Pediatrics international. Volume 57:Issue 6(2015)
• Page Start: 1192
• Page End: 1195
• Publication Date: 2015-11-05
• Subjects: anomaly -- bacterial meningitis -- immunodeficiency -- Mondini dysplasia -- pneumococcal vaccine; Pediatrics -- Periodicals; 618.92
• DOI: 10.1111/ped.12731
• Languages: English
• ISSNs: 1328-8067

Abstract

Abstract: Mondini dysplasia is rare, but has an important association with recurrent bacterial meningitis. We herein describe the case of a 3‐year‐old girl with unilateral sensorineural hearing loss who presented with three independent episodes of bacterial meningitis within 8 months. Temporal bone computed tomography indicated the characteristic features of Mondini dysplasia in the right inner ear. This was treated by surgical closure of the inner ear defect via oval window and additional vaccination was administered. Appropriate vaccination might prevent the recurrent bacterial meningitis associated with Mondini dysplasia.