Right ventricular endomyocardial fibrosis mimicking Ebstein anomaly in a patient with Behçet's disease: case report and review of the literature. Issue 3 (May 2014)

• Record Type: Journal Article
• Authors: Buturak, Ali; Saygili, Ozlem; Ulus, Sıla; Kalfa, Melike; Karabulut, Hasan; Alhan, Cem; Dagdelen, Sinan; Aksu, Kenan
• Is Part Of: Modern rheumatology. Volume 24:Issue 3(2014)
• Page Start: 532
• Page End: 536
• Publication Date: 2014-05
• Subjects: Rheumatology -- Periodicals; 616.723005
• DOI: 10.3109/14397595.2013.874731
• Languages: English
• ISSNs: 1439-7595

Abstract

<abstract> <title>Abstract</title> <p>Behçet's disease is a multisystemic, chronic inflammatory disorder with diffuse clinical manifestations including the cardiovascular system. Endomyocardial fibrosis is a rarely seen complication of Behçet's disease leading to progressive heart failure. We report a case of right ventricular endomyocardial fibrosis mimicking Ebstein anomaly in a 26-year-old male Turkish patient with Behçet's disease, who had heart failure symptoms. In addition, the previously reported cases of endomyocardial fibrosis complicating Behçet's disease are reviewed in this article.</p> </abstract>