A Coronary–Pulmonary Artery Fistula with Giant Aneurysm in a Child with Ventricular Septal Defect with Pulmonary Atresia. Issue 4 (24th December 2013)

• Record Type: Journal Article
• Authors: Mahimaiha, Jayaranganath; Patra, Soumya; Mandikal Kodanda Rama Sastry, Usha; Subramaniam, Anand; Agrawal, Navin; Nanjappa, Manjunath Cholenahally
• Is Part Of: Echocardiography. Volume 31:Issue 4(2014)
• Page Start: E130
• Page End: E131
• Publication Date: 2013-12-24
• Subjects: Echocardiography -- Periodicals; Echocardiography -- Periodicals; 616.1207543
• DOI: 10.1111/echo.12496
• Languages: English
• ISSNs: 0742-2822

Abstract

<abstract abstract-type="short" xml:lang="en" id="echo12496-abs-0001"> <title>Mini‐Abstract</title> <p>Pulmonary atresia with ventricular septal defect accounts for about 2% of all congenital heart diseases. Aortopulmonary collaterals are the usual source of pulmonary blood flow. Coronary–pulmonary artery fistula is a rare and sole source of pulmonary blood flow. We are reporting a case of a 6‐year‐old girl who presented with severe cyanosis, clubbing, and effort intolerance. Echocardiography demonstrated a large subaortic ventricular septal defect and pulmonary atresia with confluent pulmonary arteries. It also revealed the presence of a coronary–pulmonary artery fistula along with a giant coronary artery aneurysm. These findings were confirmed by an aortic root angiogram. She was referred for intra‐ cardiac repair.</p> </abstract>