Cystic lymphangiomatosis with severe intra‐abdominal bleeding in a newborn: Case report. Issue 4 (22nd June 2012)

• Record Type: Journal Article
• Authors: Baskın, Didem; Narcı, Adnan; Okur, Nazan; Uğraş, Meltem; Nadirgil Köken, Gülengül; Ali Tuncer, Ahmet; Tokyol, Çiğdem; Çetinkurşun, Salih
• Is Part Of: Journal of clinical ultrasound. Volume 41:Issue 4(2013:May)
• Page Start: 261
• Page End: 264
• Publication Date: 2012-06-22
• Subjects: Ultrasonics in medicine -- Periodicals; 616.07543
• DOI: 10.1002/jcu.21956
• Languages: English
• ISSNs: 0091-2751

Abstract

<abstract abstract-type="main" xml:lang="en"> <title>Abstract</title> <p>We report the case of a newborn girl with intestinal cystic lymphangiomatosis who presented with abdominal distension and intra‐abdominal bleeding following a prenatal ultrasound diagnosis of intestinal anomaly. Postnatal abdominal ultrasound revealed disseminated submucosal and intramural cystic dilatations of various sizes in the bowel and intestinal lymphangiomatosis was diagnosed. The presence of severe bleeding diathesis and widespread disease led to conservative treatment. The patient died on postnatal day 7 and postmortem examination confirmed cystic lymphangiomatosis. Detection of intestinal hyperechogenicity and/or dilatation in prenatal ultrasonography and the persistence of these findings during pregnancy are suggestive for pathologies such as meconium ileus, meconium peritonitis, and intestinal atresia. Although rare, intestinal lymphangiomatosis should be kept in mind in patients whose prenatal sonographic findings persist until birth. © 2012 Wiley Periodicals, Inc. J Clin Ultrasound, 2013</p> </abstract>