Pediatric Primary Follicular Mucinosis: Further Evidence of its Relationship with Mycosis Fungoides. Issue 6 (14th March 2013)

• Record Type: Journal Article
• Authors: Santos‐Briz, Angel; Cañueto, Javier; García‐Dorado, Jesus; Teresa Alonso, M.; Balanzategui, Ana; González‐Díaz, Marcos
• Is Part Of: Pediatric dermatology. Volume 30:Issue 6(2013)
• Page Start: e218
• Page End: e220
• Publication Date: 2013-03-14
• Subjects: Pediatric dermatology -- Periodicals; Children -- Diseases -- Periodicals; 618.925
• DOI: 10.1111/pde.12061
• Languages: English
• ISSNs: 0736-8046

Abstract

<abstract abstract-type="main" xml:lang="en" id="pde12061-abs-0001"> <title>Abstract</title> <p>Follicular mucinosis (FM) is an uncommon reaction pattern in which the accumulation of mucin in the follicular epithelium is the main pathologic finding. FM may be idiopathic (primary follicular mucinosis [PFM]), in association with mycosis fungoides or cutaneous T‐cell lymphoma, or in association with other neoplastic and inflammatory conditions. Herein we report a case of PFM with identical T‐cell clone rearrangement at anatomically distinct sites, supporting the idea that some authors have proposed, that FM may represent a low‐grade lymphoproliferative disease related to mycoses fungoides with favorable prognosis.</p> </abstract>