Efficacy of Ventricular Pacing in the Treatment of an Arrhythmic Storm Associated with a Congenital Long QT Mutation. (18th October 2012)

• Record Type: Journal Article
• Authors: Aziz, Peter F.; Shah, Maully J.
• Is Part Of: Congenital heart disease. Volume 8:Number 6(2013)
• Page Start: E165
• Page End: E167
• Publication Date: 2012-10-18
• Subjects: Congenital heart disease -- Periodicals; 616.1204305
• DOI: 10.1111/chd.12014
• Languages: English
• ISSNs: 1747-079X

Abstract

<abstract abstract-type="main"> <title>Abstract</title> <p>Long QT syndrome in the infant with 2:1 atrioventricular block is a malignant form of disease associated with frequent torsade de pointes in some cases. Those patients that do not respond to antiarrhythmic therapy are particularly challenging to manage. Ventricular pacing in this patient population has been shown to reduce arrhythmic events. We report a case of a newborn with frequent torsade de pointes requiring defibrillation and cardiopulmonary resuscitation with immediate shortening of the QTc interval with ventricular pacing and subsequent resolution of torsade de pointes.</p> </abstract>